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KMID : 0352120120280010027
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Journal of Kyung Hee University
2012 Volume.28 No. 1 p.27 ~ p.30
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Kidney Transplantation in a Patient with Fechtner’s Syndrome
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Kang Hwa-Ja
Kim Hyung-Gon
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Abstract
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This case report describes the successful management of a patient who has Fechtner’s syndrome, as diagnosed from clinical signs and laboratory findings. The decrease in platelet counts associated with Fechtner’s syndrome was severe in the present case (6,000/μL). Moreover, clinical manifestations of Fechtner’s syndrome were present in the patient.
The measures that we used to minimize Fechtner’s syndrome associated risks were based on a treatment proposed in relation to hemostatic defects and bleeding disorders and on principles of transfusion medicine.(8) Cryoprecipitate was precluded because of the known high risk of viral exposure.(8) Fresh frozen plasma has been suggested as a means to increase coagulation factors and to normalize bleeding time. But, Fresh frozen plasma was not transfused because of it’s
infectivity.(8) Crossmatched platelets were used because of the low platelet counts.(8-10) In keeping with the literature,(8-10) both leukodepletion and ultraviolet irradiation were performed to prevent further transfusionrelated reactions.
In conclusion, we describe herein the management of a patient with Fechtner’s syndrome involving transfusion of platelets, tranexamic acids which produced safe and effective results during kidney transplantation and postoperative time.(8-11) This protocol prevented excessive bleeding and it reduced the need for transfusion of blood products. Our technique of patient management may be an option in patients with Fechtner’s syndrome undergoing other types of surgery.
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KEYWORD
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Fechtner’s syndrome, Kidney transplantation, Platelet transfusion
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